Familial non-cystic fibrosis mucus inspissation of respiratory tract.

Arch Dis Child. 1975 September; 50(9): 727–730.

PMCID: PMC1545639

M Perlman, J Williams, M Hirsch, and J Bar-Ziv

Abstract

Perlman, M., Williams, J., Hirsch, M., and Bar-Ziv, J. (1975). Archives of Disease in Childhood, 50, 727. Familial non-cystic fibrosis mucus inspissation of respiratory tract. Two sibs, whose parents are first cousins, have had chronic obstructive airways disease from birth with recurrent otitis media, sinusitis, and mastoiditis. The disease, associated with clinically abnormal mucus, differs from other familial obstructive airways diseases and probably constitutes a new entity.

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Selected References

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Cogswell, JJ; Risdon, RA; Taylor, B. Chronic suppurative lung disease in sisters mimicking cystic fibrosis. Arch Dis Child. 1974 Jul;49(7):520–524. [PubMed]
DI SANT'AGNESE, PA. Bronchial obstruction with lobar atelectasis and emphysema in cystic fibrosis of the pancreas. Pediatrics. 1953 Aug;12(2):178–190. [PubMed]
SHWACHMAN, H; PRYLES, CV; GROSS, RE. Meconium ileus; a clinical study of twenty surviving patients. AMA J Dis Child. 1956 Mar;91(3):223–244. [PubMed]