WHO Classification (Part One)  
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Table 13. WHO Classification of Hematopoietic & Lymphoid Neoplasmas
with ICD-O Codes

NOTE: Only major disease categories are listed.
{} indicates an alternative description of the neoplasm

MYELOID NEOPLASMS
ICD-O WHO TERM
  Myeloproliferative diseases
9875/3     Chronic myelogenous leukemia, Philadelphia chromosome positive
      {t(9;22)(q34;q11)}, {BCR/ABL}
9963/3     Chronic neutrophilic leukemia
9964/3     Chronic eosinophilic leukemia/hypereosinophilic syndrome
9961/3     Chronic idiopathic myelofibrosis
9950/3     Polycythemia vera
9962/3     Essential thrombocythemia
9975/1     Myeloproliferative disease, unclassifiable
  Myelodysplastic/myeloproliferative diseases
9945/3     Chronic myelomonocytic leukemia
9876/3     Atypical chronic myelogenous leukemia
9946/3     Juvenile myelomonocytic leukemia
  Myelodysplastic syndromes
9980/3     Refractory anemia
9982/3     With ringed sideroblasts
9980/3     Without ringed sideroblasts
9985/3     Refractory cytopenia (myelodysplastic syndrome) with     multilineaage dysplasia
9983/3     Refractory anemia (myelodysplastic syndrome) with excess blasts
9986/3     5q- (5q deletion) syndrome
9989/3     Myelodysplastic syndrome, unclassifiable
  Acute myeloid leukemias (AMLs)
      AMLs with recurrent cytogenetic translacations
9896/3         AML with {t(8;21)(q22;q22)}, {AML1(CBF-alpha)/ETO}
9866/3         Acute promyelocytic leukemia {AML with with         t(15;17)(q22;q11-12} and variants,
           {PML/RAR-alpha}
9871/3         AML with abnormal bone marrow eosinophils {inv(16)(p13q22)}         or
           {t(16;16)(p13;q11)}, {CBFb/MYH11}
9897/3         AML with 11q23 abnormalities {MLL}
9895/3     AML with multilineage dysplasia
9895/3         With prior myelodysplasic syndrome
9895/3         Without prior myelodysplastic syndrome
9920/3     AML and myelodysplastic syndromes, therapy-related
9920/3         Alkylating agent-related
9920/3         Epipodophyllotoxin-related (some may be lymphoid)
9920/3         Other types
9861/3     AML not otherwise categoriezed
9872/3         AML minimally differentiated
9873/3         AML without maturation
9874/3         AML with maturation
9867/3         Acute myelomonocytic leukemia
9891/3         Acute monocytic leukemia
9840/3         Acute erythroid leukemia
9910/3         Acute megakaryocytic leukemia
9870/3         Acute basophilic leukemia
9931/3         Acute panmyelosis with myelofibrosis
9805/3 Acute biphenotypic leukemias

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